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Dernières publications
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Julia Pereira Lemos, Liliane Patrícia Gonçalves Tenório, Vincent Mouly, Gillian Butler-Browne, Daniella Arêas Mendes-Da-Cruz, et al.. T cell biology in neuromuscular disorders: a focus on Duchenne Muscular Dystrophy and Amyotrophic Lateral Sclerosis. Frontiers in Immunology, 2023, 14, pp.120283. ⟨10.3389/fimmu.2023.1202834⟩. ⟨hal-04603915⟩
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Fanny Roth, Jamila Dhiab, Alexis Boulinguiez, Hadidja-Rose Mouigni, Saskia Lassche, et al.. Assessment of PABPN1 nuclear inclusions on a large cohort of patients and in a human xenograft model of oculopharyngeal muscular dystrophy. Acta Neuropathologica, 2022, ⟨10.1007/s00401-022-02503-7⟩. ⟨hal-03832636⟩
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Elisa Negroni, Maria Kondili, Laura Muraine, Mona Bensalah, Gillian Sandra Butler-Browne, et al.. Muscle fibro-adipogenic progenitors from a single-cell perspective: Focus on their “virtual” secretome. Frontiers in Cell and Developmental Biology, 2022, 10, ⟨10.3389/fcell.2022.952041⟩. ⟨hal-03830589⟩
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Chiffres clés
103
Publications avec texte intégral
Open Access
61 %
Mots clés
Muscle strength
Metabolism
FSHD
Agrégats de PABPN1
Accelerometry
Dystrophie musculaire oculopharyngée
Aav-U7
BINDING SPECIFICITY
Muscle stem cells
Antisens oligonucleotides
Xenograft
Myoblast
Biomarker
Adipose tissue
Myotube
Myositis
Cell therapy
Muscle
Triplet expansion disease
DNA methylation
Fibrosis
Ageing
GENE
Calcium
Akt
Omics
Alzheimer's disease
Autologous
Bile salt hydrolases
Autoimmune diseases
AUTOPHAGY
Annexin A2
Dystrophin
Regulatory T cells
Neuromuscular disease
Regenerative medicine
Cross-bridge kinetics
Pharyngeal muscle
Gene replacement
Gene therapy
AAV
AAV vectors
Myogenesis
ALS
Aggregate
Exon-skipping
Anti-fibrotic pharmacotherapies
Geriatric assessment
Haploinsufficiency
Mass spectrometry
Antiserum
Skeletal muscle
Functional genomics
Inflammation
Andermann syndrome
DMD
Neuromuscular junction NMJ
FAPs
Anti-acetylcholine receptor antibodies
Duchenne muscular dystrophy
PABPN1 agregates
Intercellular communication
Thérapie génique
RNA
Myoblasts
Satellite cells
OPMD
Nuclear envelope
PABPN1
Differentiation
Sarcopenia
Pax7
Transcriptomics
Arbovirus
Atrophy
Actin
ARN
Human
Myopathies
Effector T cells
AChR antibodies
Oculopharyngeal muscular dystrophy
Aged
Amyotrophic Lateral Sclerosis
Dysferlin
Myosin
MUTATIONS
DUX4
Lamins
Dysferlinopathy
Satellite cell
Muscle fibrosis
Regeneration
APOPTOSIS
Myopathy
2-D PAGE
Muscular dystrophy
Muscle dystrophy
Alphavirus
Epigenetics